Langerhans-cell histiocytosis

Term ID

DOID:2571

Synonyms

• Histiocytosis X
• Langerhan's cell histiocytosis
• Langerhans cell granulomatosis
• Letterer-Siwe disease
• Letterer-Siwe disease involving intra-abdominal lymph nodes
• Letterer-Siwe disease involving intrapelvic lymph nodes
• Letterer-Siwe disease involving intrathoracic lymph nodes
• Letterer-Siwe disease involving lymph nodes of axilla and upper limb
• Letterer-Siwe disease involving lymph nodes of head, face and neck
• Letterer-Siwe disease involving lymph nodes of head, face, and neck
• Letterer-Siwe disease involving lymph nodes of inguinal region and lower limb
• Letterer-Siwe disease involving lymph nodes of multiple sites
• Letterer-Siwe disease involving spleen
• Letterer-Siwe disease of intra-abdominal lymph nodes
• Letterer-Siwe disease of intrapelvic lymph nodes
• Letterer-Siwe disease of intrathoracic lymph nodes
• Letterer-Siwe disease of lymph nodes of axilla and upper limb
• Letterer-Siwe disease of lymph nodes of axilla and/or upper limb
• Letterer-Siwe disease of lymph nodes of head, face and neck
• Letterer-Siwe disease of lymph nodes of head, face and/or neck
• Letterer-Siwe disease of lymph nodes of inguinal region amd/or lower limb
• Letterer-Siwe disease of lymph nodes of inguinal region and lower limb
• Letterer-Siwe disease of lymph nodes of inguinal region and/or lower limb
• Letterer-Siwe disease of lymph nodes of multiple sites
• Letterer-Siwe disease of spleen

Definition

A histiocytosis that is characterized by clonal proliferation of Langerhans cells. http://en.wikipedia.org/wiki/Langerhans_cell_histiocytosis

References

• ICD10CM:C96.0
• ICD10CM:C96.6
• ICD9CM:202.5
• ICDO:9751/1
• MESH:C538636
• MESH:D006646
• MIM:246400
• MIM:604856
• NCI:C3107
• NCI:C3160
• SNOMEDCT_US_2023_03_01:154583006
• SNOMEDCT_US_2023_03_01:234439008
• UMLS_CUI:C0019621
• UMLS_CUI:C0023381

Ontology

Human Disease   ( DOID:2571 )