(R)-2-hydroxy-4-methylpentanoic acid

Term ID

CHEBI:55534

Synonyms

(2R)-2-hydroxy-4-methylpentanoic acid
(R)-2-hydroxy-4-methylpentanoic acid
(R)-2-hydroxy-4-methylvaleric acid
(R)-2-hydroxyisocaproic acid
(R)-leucic acid
2-hydroxy-4-methyl-D-valeric acid
alpha-Hydroxyisocaproic acid
D-2-hydroxy-4-methylpentanoic acid
D-2-hydroxy-4-methylvaleric acid
D-2-hydroxyisocaproic acid
D-leucic acid
delta-leucic acid
leucic acid

Definition

The (R)-enantiomer of 2-hydroxy-4-methylpentanoic acid. Found in patients with short-bowel syndrome (an inborn error of metabolism), and in maple syrup urine disease, MSUD.

References

Beilstein:1721731
CAS:20312-37-2
KEGG:C03264
PMID:9766851

Ontology

ChEBI ( EBI )

Relationships

is a type of: (2R)-2-hydroxy monocarboxylic acid 2-hydroxy-4-methylvaleric acid

(2R)-2-hydroxy monocarboxylic acid 2-hydroxy-4-methylvaleric acid Show first 5 Terms
inverse has_functional_parent: (R)-2-hydroxy-4-methylpentanoyl-CoA

(R)-2-hydroxy-4-methylpentanoyl-CoA Show first 5 Terms
inverse is_conjugate_base_of: (R)-2-hydroxy-4-methylpentanoate

(R)-2-hydroxy-4-methylpentanoate Show first 5 Terms
inverse is_enantiomer_of: (S)-2-hydroxy-4-methylpentanoic acid

(S)-2-hydroxy-4-methylpentanoic acid Show first 5 Terms
is_conjugate_acid_of: (R)-2-hydroxy-4-methylpentanoate

(R)-2-hydroxy-4-methylpentanoate Show first 5 Terms
is_enantiomer_of: (S)-2-hydroxy-4-methylpentanoic acid

(S)-2-hydroxy-4-methylpentanoic acid Show first 5 Terms

Phenotype

Phenotype resulting from (R)-2-hydroxy-4-methylpentanoic acid

Phenotype where environments contain (R)-2-hydroxy-4-methylpentanoic acid

Phenotype modified by environments containing (R)-2-hydroxy-4-methylpentanoic acid

Human Disease Model