PUBLICATION

A novel FTY720 analogue targets SET-PP2A interaction and inhibits growth of acute myeloid leukemia cells without inducing cardiac toxicity

Authors
Vicente, C., Arriazu, E., Martínez-Balsalobre, E., Peris, I., Marcotegui, N., García-Ramírez, P., Pippa, R., Rabal, O., Oyarzábal, J., Guruceaga, E., Prósper, F., Mateos, M.C., Cayuela, M.L., Odero, M.D.
ID
ZDB-PUB-191011-11
Date
2019
Source
Cancer letters   468: 1-13 (Journal)
Registered Authors
Keywords
Acute myeloid leukemia, FTY720, PP2A, SET, cardiac toxicity
MeSH Terms
  • Adult
  • Aged
  • Aged, 80 and over
  • Animals
  • Apoptosis/drug effects
  • Cardiotoxicity/etiology
  • Cardiotoxicity/prevention & control*
  • Cell Line, Tumor
  • Cell Proliferation/drug effects
  • DNA-Binding Proteins/metabolism*
  • Female
  • Fingolimod Hydrochloride/administration & dosage*
  • Fingolimod Hydrochloride/analogs & derivatives
  • Fingolimod Hydrochloride/toxicity
  • Heart Rate/drug effects
  • Histone Chaperones/metabolism*
  • Humans
  • Leukemia, Myeloid, Acute/drug therapy*
  • Leukemia, Myeloid, Acute/pathology
  • Male
  • Middle Aged
  • Protein Binding/drug effects
  • Protein Phosphatase 2/metabolism*
  • Toxicity Tests, Acute
  • Xenograft Model Antitumor Assays
  • Zebrafish
PubMed
31593801 Full text @ Cancer Lett.
Abstract
Acute myeloid leukemia (AML) is an aggressive disease associated with very poor prognosis. Most patients are older than 60 years, and in this group only 5-15% of cases survive over 5 years. Therefore, it is urgent to develop more effective targeted therapies. Inactivation of protein phosphatase 2A (PP2A) is a recurrent event in AML, and overexpression of its endogenous inhibitor SET is detected in ∼30% of patients. The PP2A activating drug FTY720 has potent anti-leukemic effects; nevertheless, FTY720 induces cardiotoxicity at the anti-neoplastic dose. Here, we have developed a series of non-phosphorylable FTY720 analogues as a new therapeutic strategy for AML. Our results show that the lead compound CM-1231 re-activates PP2A by targeting SET-PP2A interaction, inhibiting cell proliferation and promoting apoptosis in AML cell lines and primary patient samples. Notably, CM-1231 did not induce cardiac toxicity, unlike FTY720, in zebrafish models, and reduced the invasion and aggressiveness of AML cells more than FTY720 in zebrafish xenograft models. In conclusion, CM-1231 is safer and more effective than FTY720; therefore, this compound could represent a novel and promising approach for treating AML patients with SET overexpression.
Genes / Markers
Figures
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Phenotype
Mutations / Transgenics
Human Disease / Model
Sequence Targeting Reagents
Fish
Antibodies
Orthology
Engineered Foreign Genes
Mapping