Term Name: | primary intracranial sarcoma, DICER1-mutant |
---|---|
Synonyms: | |
Definition: | A brain sarcoma that is composed of malignant pleomorphic or spindle neoplastic cells typically demonstrating myogenic and/or chondroid differentiation. Cytoplasmic eosinophilic globules and myxoid stroma formation are usually present. It is associated with mutations in the DICER1 gene. |
Ontology: | Human Disease [DOID:0081316] ( DOID:0081316 ) |